Table 1

Characteristics of the six patients with congenital bilateral perisylvian syndrome

Age (years)SexEpilepsy onset-offset age (years)Tongue lateral movements right/leftLip movements right/leftFinger movements right/leftGross motor skills right/leftIntellectual capacityPMG location on MRI
F, female; M, male; +, normal; −, absent; ±, borderline; (−), mild disability; c, clumsy; w, weak; PMG, polymicrogyria; MRI, magnetic resonance imaging; bi, bilateral; Fop, frontal opercular; FP, frontoparietal; Syl, perisylvian
P168Fno−/−w/wc/c+/+±bi FP, bi Syl
P210Mno−/−w/wc/c+/++bi FP, bi Syl
P312M14−/−−/−c/c+/+(−)bi FP, bi Syl
P413M10, 1 sz−/−w/wc/c+/++bi FP, bi Syl
P515Fno−/+w/++/++/+±bi Syl
P620F3–12−/−+/++/−+/++bi Fop, right FP right Syl