Table 2

 The main outcome measures in the three patient groups

FSHD (n = 139)MD (n = 322)HMSN-I (n = 137)p Value
Values are mean (SD). A higher value indicates more complaints or impairments.
*Significantly different from FSHD, Bonferroni p<0.05.
†Significantly different from MD, Bonferroni p<0.05.
‡Significantly different from HMSN-I, Bonferroni p<0.05.
FSHD, facioscapulohumeral muscular dystrophy; HMSN-I, hereditary motor and sensory neuropathy type I; MD, adult onset myotonic dystrophy; SF-36, 36 item short form general health questionnaire.
CIS
    CIS-fatigue36.5 (12.5)†40.4 (11.8)*‡37.4 (12.2)†0.002
    CIS-concentration12.3 (8.2)†16.8 (8.3)*‡13.8 (8.7)†0.000
    CIS-motivation12 (5.9)†16.8 (6.6)*‡12.2 (6.1)†0.000
    CIS-activity10.1 (5.5)†13.2 (5.6)*‡9.4 (5.5)†0.000
SF-36
    physical functioning45.2 (31.4)48.4 (28.2)53.1 (26.4)NS
    social functioning71.6 (24.2)69.9 (24.3)67.5 (24.3)NS
    role limitations physical47.9 (42)48.2 (39.7)48.9 (39)NS
    role limitations emotional69.5 (41.6)73.9 (37.6)67.4 (41.6)NS
    mental health72.6 (17)72.7 (18)68.9 (19.2)NS
    bodily pain66.6 (23.8)†75.4 (25.3)*‡68.5 (25.5)†0.001
    general health perception51.7 (21.6)†40.5 (22.3)*‡52.5 (20.7)†0.000