Table 1

 Patients with multiple system atrophy who initially presented with laryngeal abductor paralysis/stridor

Patient*Years from the onset of illnessLaryngoscopy findings†
012345678910111213
*Age, sex, diagnosis.
†Laryngeal abductor paralysis: +(mild), ++(moderate), +++(severe), Isozaki’s classification.
AHI, apnoea hypopnoea index; BD, bladder dysfunction; CPAP, continuous positive airway pressure; F, female; HUT, head up tilt (60° for 10 min); M, male; MSA-C, cerebellar form of multiple system atrophy; MSA-P, parkinsonian form of multiple system atrophy; ODI, oxygen desaturation index (dips per hour); PH, postural hypotension; RBD, REM sleep behavioural disorder; SAS, sleep apnoea syndrome.
1. 62/M MSA-PLaryngeal stridorBDDecreased sweatingAkinesia, cerebellar ataxia, PH Admission: tracheotomy ++
2. 74/F MSA-PLaryngeal stridorConstipation, BD, PH, akinesiaAdmission: inspiratory gasp, hoarseness+++
3. 83/F MSA-CLaryngeal stridor, inspiratory gaspAtaxic gait, BD, constipationPH Admission: tracheotomy AkinesiaPneumonia, Admission:gastrostomy+++
4. 59/F MSA-CLaryngeal stridor, RBDAtaxic gaitBD Admission: CPAP >tracheotomy ++
5. 62/M MSA-CLaryngeal stridorConstipation, BDAdmission: ataxic gait, akinesia, inspiratory gasp; CPAP Admission: tracheotomy +++
6. 57/F MSA-PLaryngeal stridor, hoarsenessHand tremorDysphasiaakinesia, ataxic gait, BD Admission: laser incision >tracheotomy +++
7. 53/M MSA-PLaryngeal stridor, hoarseness, BD, erectile dysfunction, constipationPH, decreased sweating, ataxic gaitAdmission: dysphagia++
8. 63/F MSA-CLaryngeal stridor, ataxic gaitAdmission hoarseness, akinesia; CPAP+++