First assessment | Second assessment | |
---|---|---|
*n = 8 in both sections of the table. | ||
Mild decline: NART–FIQ = 10; moderate decline: NART–FIQ = 11 to 20; severe decline: NART–FIQ >20. | ||
A. Level of intellectual decline in the inherited prion disease group | ||
VIQ | ||
None | 2 | 1 |
Mild decline | 1 | – |
Moderate decline | 1 | 3 |
Severe decline | 4 | 4 |
PIQ | ||
None | 1 | 1 |
Mild decline | – | – |
Moderate decline | 2 | 2 |
Severe decline | 5 | 5 |
FIQ | ||
None | 1 | 1 |
Mild decline | – | – |
Moderate decline | 2 | 2 |
Severe decline | 5 | 5 |
B. Number of impaired cases with inherited prion disease | ||
Memory (words) | 4 | 6 |
Memory (faces) | 6 | 7 |
Nominal skills | 3 | 4 |
Visual perception | 4 | 4 |
Frontal | 7 | 8 |