Variable | sALS | homD90A | Control | |||
---|---|---|---|---|---|---|
ALSFRS-R, revised amyotrophic lateral sclerosis functional rating scale; homD90A, homozygous D90A SOD1 ALS; sALS, sporadic amyotrophic lateral sclerosis; UMN, upper motor neurone. Values are mean (SD where applicable). | ||||||
n | 28 | 11 | 24 | |||
Sex (M:F) | 21:7 | 3:8 | 13:11 | |||
Age | 58 (9) | 52 (12) | 41 (13) | |||
9 | 12 | 13 | ||||
ALSFRS-R | 37 (5) | 34 (8) | – | |||
5 | 8 | – | ||||
UMN score | 8 (6) | 9 (3) | NA | |||
6 | 3 | |||||
Duration (months) | 29 (18) | 65 (57) | NA | |||
18 | 57 |