1‡ | 34/M | Plasma exchange | Oral prednisolone | Cyclophosphamide pulse | Ciclosporin | | Stabilised for 26 months | 51 | 0 |
| | Temporarily responded | Temporarily responded, relapsed during tapering | Unchanged | Responded | | | | |
2 | 47/M | Plasma exchange | Oral prednisolone | No therapy required | | | Complete remission | 42 | 0 |
| | Temporarily responded | Responded | | | | (40 months) | | |
3 | 59/F | Plasma exchange | Oral prednisolone | No therapy required | | | Complete remission | 39 | 0 |
| | Temporarily responded | Responded | | | | (34 months) | | |
4 | 62/M | Plasma exchange | Oral prednisolone | No therapy required | | | Complete remission | 67 | 0 |
| | Temporarily responded | Responded | | | | (32 months) | | |
5 | 46/M | IVIg | Oral prednisolone | No therapy required | | | Complete remission | 36 | 0 |
| | Rapidly responded | Responded | | | | (29 months) | | |
6 | 52/M | IVIg | Oral prednisolone | No therapy required | | | Complete remission | 28 | 0 |
| | Rapidly responded | Responded | | | | (28 months) | | |
7 | 44/F | IVIg | Oral prednisolone | No therapy required | | | Complete remission | 46 | 0 |
| | Slowly responded | Responded | | | | (24 months) | | |
8 | 11/M | IVIg | Oral prednisolone | No therapy required | | | Complete remission | 30 | 0 |
| | Rapidly responded | Responded | | | | (18 months) | | |
9 | 53/M | IVIg | Oral prednisolone | Cyclophosphamide pulse | Ciclosporin | Tacrolimus | Stabilised for 12 months; | 66 | 12 |
| | Temporarily responded | Unchanged, relapsed during tapering | Unchanged | Unchanged | Unchanged | maintained IVIg | | |
10 | 45/F | IVIg | Oral prednisolone | Ciclosporin | | | Stabilised for 9 months; | 37 | 6 |
| | Temporarily responded | Temporarily responded, relapsed during tapering | Responded | | | maintained IVIg; no further relapses | | |
11 | 34/F | IVIg | Oral prednisolone | Ciclosporin | | | Stabilised for 20 months; | 45 | 7 |
| | Temporarily responded | Temporarily responded, relapsed during tapering | Responded | | | no IVIg required; no further relapses | | |
12 | 65/F | IVIg | Oral prednisolone | Ciclosporin | | | Stabilised for 18 months; | 48 | 4 |
| | Temporarily responded | Unchanged, progressed | Responded | | | no IVIg required; no further relapses | | |
13 | 19/F | IVIg | Oral prednisolone | | | | Stabilised for 12 months; | 31 | 4 |
| | Rapidly responded | Responded | | | | no IVIg required | | |
14 | 45/M | IVIg | Oral prednisolone | | | | Stabilised for 11 months; | 42 | 6 |
| | Rapidly responded | Responded | | | | no IVIg required | | |
15 | 37/M | IVIg | Oral prednisolone | | | | Stabilised for 6 months; | 37 | 3 |
| | Rapidly responded | Responded | | | | no IVIg required | | |