Table 1

 Prognosis of amyotrophic lateral sclerosis with respiratory onset

Mean survival time fromMean (months)SD
FVC, forced vital capacity; NIPPV, non-invasive positive pressure ventilation; PAV, permanent assisted ventilation.
Symptom onset to death30.620.1
Symptom onset to death or PAV2714.9
Diagnosis to death13.416.7
Diagnosis to death or PAV9.89.7
Symptom onset to death (NIPPV offered and tolerated)36.416
Symptom onset to death (no NIPPV)21.516
Onset to death/PAV if initial FVC was <50% (n = 6)29.514.1
Onset to death/PAV if initial FVC was >50% (n = 15)2615.6