Incident cohort (n = 465)* | Prevalent cohort (n = 200)† | |
Median age (y) | 66.0 | 61.8 |
Sex (M:F) (%) | 268 (57.6):197 (42.4) | 120 (60.0):80 (40.0) |
Limb:bulbar:generalised onset (%) | 268 (57.6): 164 (35.3): 33 (7.1) | 137 (68.5): 63 (31.5): 0 |
Patients younger than 55 y (%) | 93 (20.0) | 67 (33.5) |
Patients older than 65 y (%) | 244 (52.5) | 74 (37.0) |
Family history of ALS (%) | 29 (6.2) | 11 (10.5) |
Second diagnosis of FTD (%) | 32 (6.9) | 12 (6.0) |
Mean diagnostic delay (months) | 13.0 | 22.7 |
Median survival (months) | 16.4 | 120.9 |
*1995–1997 and 2002–2004 cohorts combined.
†On 31 December 2003.
ALS, amyotrophic lateral sclerosis; FTD, frontotemporal dementia.