Table 1 Epidemiological features of moyamoya disease
Present studyPrevious study—19972
Number of cases2671176
Detection rate (per 100 000)0.940.35
Prevalence (per 100 000)10.53.16
Sex ratio (male:female)1:2.21:1.8
Patients younger than 10 years old at onset (%)15.1%47.8%
Pattern of age distribution2 peaks2 peaks
Highest peak in age distribution (in years)45–4910–14
Second peak in age distribution (in years)5–940–49
Patients with family history15.4%10.0%