Table 4 Spearman’s coefficients of correlation between activity limitations and MMT
DMD/BMD LGMD (n = 45)HN (n = 44)MD (n = 37)FSHD (n = 11)SMA (n = 14)ALS (n = 18)Total sample (n = 245)
Upper limb proximal muscles
    Shoulder flexion0.73**0.270.230.590.450.51*0.47**
    Shoulder abduction0.61**0.200.300.66*0.250.380.43**
    Elbow flexion0.75**0.250.240.530.59*0.100.48**
    Elbow extension0.68**0.260.39*0.400.290.050.40**
Upper limb distal muscles
    Wrist flexion0.43*−0.160.42**0.010.88**0.180.27**
    Wrist extension0.45*−0.020.34*0.100.88**0.060.34**
    Finger flexion0.62**0.030.35*0.010.93**−0.020.17*
    Finger extension0.73**−0.070.53**0.350.94**0.100.31**
    Interossei0.63**0.210.46**−0.500.95**0.200.25**
Lower limb proximal muscles
    Hip extension0.59**0.040.190.500.73*0.370.39**
    Hip abduction0.58**0.250.010.280.560.390.46**
    Hip flexion0.71**−0.030.160.470.460.450.44**
    Knee extension0.68**0.020.35*0.69*0.580.420.45**
    Knee flexion0.72**0.45*0.180.590.73*0.66*0.50**
Lower limb distal muscles
    Ankle dorsiflexion0.56**0.280.40*0.84**0.65*0.360.34**
    Ankle plantar flexion0.75**0.280.51**0.390.400.560.40**
    Toe extension0.69**0.200.39*0.77**−0.030.59*0.35**
    Toe flexion0.83**0.360.140.010.320.88**0.49**
  • ALS, amyotrophic lateral sclerosis; BMD, Becker muscular dystrophy; DMD, Duchenne muscular dystrophy; FSHD, facio-scapulo-humeral dystrophy; HN, hereditary neuropathy; LGMD, limb girdle muscular dystrophy; MD, myotonic dystrophy; MMT, Manual Muscle Testing; SMA, spinal muscular atrophy.

  • *0.05>p>0.01, **p<0.01.