Table 3

Average prevalence rates, 1990–2010, of recorded diagnoses of Huntington's disease by age group (per 100 000)

Age group (years)Average population numbersAverage HD numbersAverage prevalence (95% CIs)
21–25202 85242.0 (0.5 to 5.1)
26–30223 48873.1 (1.3 to 6.5)
31–35240 698156.2 (3.5 to 10.3)
36–40249 476239.2 (5.8 to 13.8)
41–45241 7452811.6 (7.7 to 16.7)
46–50225 0373214.2 (9.7 to 20.1)
51–55208 7453315.81 (10.9 to 22.2)
56–60193 4373015.8 (10.5 to 22.1)
61–65169 4412615.3 (10.0 to 22.5)
66–70144 2952114.6 (9.0 to 22.3)
71–75125 8121310.3 (5.5 to 17.7)
76–80102 36098.8 (4.0 to 16.7)
81–8572 09245.6 (1.5 to 14.2)
86+59 10511.7 (0 to 9.4)
  • HD, Huntington's disease.