Teased fibres | |||||||||||
---|---|---|---|---|---|---|---|---|---|---|---|
Case | Antibodies | Age* (years)/sex | Duration† | Type‡ | Sural nerve SCV (m/s) | MF density (number/mm2) | UMF density (number /mm2) | De (%) | Re (%) | Ax (%) | Axo–glial detachment (%) |
1 | NF | 15/M | 7 months | DADS | 31 | 8415 | 38 566 | 0 | 0 | 2 | 47 |
2 | NF | 26/M | 5 months | Typical | NE | 6532 | 24 880 | 1 | 3 | 3 | 77 |
3 | NF | 55/M | 7 months | Typical | NE | 5867 | 29 338 | 0 | 6 | 2 | 29 |
4 | NF | 26/M | 13 months | DADS | 35 | 6317 | 27 955 | 0 | 7 | 2 | 48 |
5 | NF | 24/F | 5 months | DADS | 48 | 6107 | 28 743 | 0 | 2 | 1 | 9 |
6 | NF | 41/M | 4 months | Typical | NE | 6029 | 24 133 | 0 | 3 | 0 | 58 |
7 | NF | 21/M | 7 months | DADS | 44 | 8162 | 30 187 | 0 | 3 | 2 | 45 |
8 | NF | 56/M | 14 months | DADS | NE | 5879 | 36 017 | 2 | 1 | 14 | 91 |
9 | NF | 57/F | 7 months | Typical | 34 | 6042 | 32 861 | 9 | 7 | 6 | 77 |
10 | CNTN | 72/M | 4 years | Typical | NE | 6023 | 27 425 | 0 | 11 | 3 | 22 |
11 | – | 32/M | 4 months | MADSAM | NE | 6664 | 29 771 | 2 | 13 | 3 | 2 |
12 | – | 44/F | 15 months | Typical | 35 | 6835 | 31 047 | 0 | 8 | 0 | 6 |
13 | – | 15/F | 2.5 months | Pure motor | 38 | 7481 | 31 260 | 0 | 2 | 0 | 0 |
14 | – | 60/M | 1 months | Typical | 47 | 6769 | 26 370 | 9 | 7 | 2 | 0 |
15 | – | 61/M | 1 month | Typical | NE | 5492 | 29 983 | 10 | 21 | 4 | 5 |
16 | – | 48/M | 2 months | MADSAM | 44 | 7441 | 22 754 | 0 | 6 | 1 | 2 |
17 | – | 50/M | 4 months | Typical | 43 | 5308 | 21 692 | 0 | 9 | 1 | 3 |
18 | – | 66/F | 7 months | Typical | NE | 4778 | 19 906 | 7 | 15 | 0 | 0 |
19 | – | 42/F | 9 months | Pure sensory | 30 | 6204 | 37 882 | 8 | 4 | 1 | 2 |
20 | – | 72/F | 13 months | DADS | 35 | 5868 | 24 636 | 5 | 38 | 0 | 11 |
21 | – | 73/F | 9 months | DADS | NE | 2116 | 23 702 | 12 | 40 | 0 | 0 |
22 | – | 38/F | 13 years | MADSAM | NE | 7627 | 29 589 | 0 | 9 | 0 | 10 |
23 | – | 66/F | 5 years | DADS | NE | 4741 | 20 857 | 0 | 6 | 6 | 3 |
*Age at biopsy.
†Duration of neuropathy until biopsy.
‡Based on the European Federation of Neurological Societies/Peripheral Nerve Society guideline.9
Ax, axonal degeneration; CNTN, contactin-1; DADS, distal acquired demyelinating symmetric; De, demyelination; MADSAM, multifocal acquired demyelinating sensory and motor; MF, myelinated fibre; NE, not elicited; NF, neurofascin-155; Re, remyelination; SCV, sensory nerve conduction velocity; UMF, unmyelinated fibre.