Table 2

Dystonia spread characteristics based on onset site

Cervical
(n=286)
Blepharospasm (n=116)Hand
(n=47)
Laryngeal
(n=38)
Spread, n (%)24 (8.4)58 (50.0)8 (17.0)6 (15.8)
No spread, n (%)262 (91.6)58 (50.0)39 (83.0)32 (84.2)
Time to first spread, mean (SD), years3.5 (2.1)2.3 (1.9)3.3 (2.0)3.1 (2.1)
First spread, body region, n (% of those who spread)
 Cervical26 (44.8)6 (75.0)6 (100)
 Blepharospasm5 (20.8)0 (0)1 (16.7)
 Hand10 (41.7)2 (3.4)0 (0)
 Laryngeal5 (20.8)2 (3.4)1 (12.5)
 Oromandibular4 (16.7)49 (84.5)0 (0)1 (16.7)
 Upper arm6 (25.0)0 (0)1 (12.5)0 (0)
 Trunk0 (0)1 (1.7)0 (0)0 (0)
 Foot1 (4.2)0 (0)0 (0)0 (0)
Any spread, body region, n (% of those who spread)
 Cervical34 (58.6)6 (75.0)6 (100)
 Blepharospasm5 (20.8)0 (0)1 (16.7)
 Hand11 (45.8)7 (12.1)2 (33.3)
 Laryngeal6 (25.0)5 (8.6)1 (12.5)
 Oromandibular5 (20.8)49 (84.5)0 (0)1 (16.7)
 Tongue1 (4.2)5 (8.6)0 (0)0 (0)
 Upper arm6 (25.0)2 (3.4)1 (12.5)0 (0)
 Trunk0 (0)2 (3.4)0 (0)0 (0)
 Foot1 (4.2)1 (1.7)0 (0)0 (0)