Reference charts for respiratory chain activities in human tissues
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Cited by (112)
Mitochondrial dysfunction caused by novel ATAD3A mutations
2020, Molecular Genetics and MetabolismAnalyzing mitochondrial function in human peripheral blood mononuclear cells
2018, Analytical BiochemistryCitation Excerpt :In Table 3, data are corrected for non-mitochondrial respiration (antimycin A respiration for protocol 1, rotenone and antimycin A respiration for protocol 2); our data using mononuclear cells for intact cellular respiration, OXPHOS (complex I), OXPHOS (complex I + complex II) and uncoupled complex I are similar to the data reported for controls in peripheral blood monocytes by the Elmer group [22,49]. Additionally, our data for OXPHOS (complex I + complex II) is similar to that derived from fresh isolated lymphocytes [50]. The rate of OXPHOS complex I + complex II was 3-fold higher than OXPHOS complex I alone.
Evaluating clinical mitochondrial respiratory chain enzymes from biopsy specimens presenting skewed probability distribution of activity data
2016, MitochondrionCitation Excerpt :This may be the reason for the variation between the reference values for the mitochondrial respiratory chain enzymes from different laboratories, forcing them to rely on reference data accumulated from their own activity measurements. Reference charts have been published, e.g. (Chretien et al., 1994), but modification and development of analytical and preparative procedures may necessitate laboratory-specific reference data banks. Obtaining reference values particularly for pediatric diagnostics is challenging (Bernier et al., 2002; Gellerich et al., 2004; Grazina, 2012; Letellier et al., 2000; Wolf and Smeitink, 2002).
Regulation of leukocyte tricarboxylic acid cycle in drug-naïve Bipolar Disorder
2015, Neuroscience Letters