Abstract
We report a patient with incapacitating POEMS syndrome characterized by serum monoclonal protein, polyneuropathy, organomegaly, endocrinopathy, mesangiocapillary glomerulonephritis, massive ascites formation, and pulmonary hypertension. A dramatic improvement in the clinical condition occurred after administration of thalidomide, a drug with known anti-angiogenetic, anti-proliferative, and anti-cytokine properties.
Copyright 2004 Wiley-Liss, Inc.
MeSH terms
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Angiogenesis Inhibitors / administration & dosage
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Angiogenesis Inhibitors / adverse effects
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Angiogenesis Inhibitors / therapeutic use*
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Diagnosis, Differential
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Exanthema / chemically induced
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Female
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Humans
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Middle Aged
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POEMS Syndrome / diagnosis
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POEMS Syndrome / drug therapy*
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Thalidomide / administration & dosage
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Thalidomide / adverse effects
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Thalidomide / therapeutic use*
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Treatment Outcome
Substances
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Angiogenesis Inhibitors
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Thalidomide