The transcription factor IRF8 activates integrin-mediated TGF-β signaling and promotes neuroinflammation

Immunity. 2014 Feb 20;40(2):187-98. doi: 10.1016/j.immuni.2013.11.022. Epub 2014 Jan 30.

Abstract

Recent epidemiological studies have identified interferon regulatory factor 8 (IRF8) as a susceptibility factor for multiple sclerosis (MS). However, how IRF8 influences the neuroinflammatory disease has remained unknown. By studying the role of IRF8 in experimental autoimmune encephalomyelitis (EAE), a mouse model of MS, we found that Irf8(-/-) mice are resistant to EAE. Furthermore, expression of IRF8 in antigen-presenting cells (APCs, such as macrophages, dendritic cells, and microglia), but not in T cells, facilitated disease onset and progression through multiple pathways. IRF8 enhanced αvβ8 integrin expression in APCs and activated TGF-β signaling leading to T helper 17 (Th17) cell differentiation. IRF8 induced a cytokine milieu that favored growth and maintenance of Th1 and Th17 cells, by stimulating interleukin-12 (IL-12) and IL-23 production, but inhibiting IL-27 during EAE. Finally, IRF8 activated microglia and exacerbated neuroinflammation. Together, this work provides mechanistic bases by which IRF8 contributes to the pathogenesis of MS.

Publication types

  • Research Support, N.I.H., Intramural

MeSH terms

  • Animals
  • Cells, Cultured
  • Dendritic Cells / immunology
  • Encephalomyelitis, Autoimmune, Experimental / physiopathology
  • Flow Cytometry
  • Inflammation / physiopathology*
  • Integrins / metabolism*
  • Interferon Regulatory Factors / genetics
  • Interferon Regulatory Factors / metabolism*
  • Macrophages / immunology
  • Mice
  • Mice, Knockout
  • RNA, Messenger / genetics
  • Signal Transduction*
  • Transforming Growth Factor beta / metabolism*

Substances

  • Integrins
  • Interferon Regulatory Factors
  • RNA, Messenger
  • Transforming Growth Factor beta
  • interferon regulatory factor-8