Lysosomal defect of hepatic copper excretion in Wilson's disease (hepatolenticular degeneration)

Gastroenterology. 1973 Jan;64(1):99-105.
No abstract available

MeSH terms

  • Adult
  • Aged
  • Common Bile Duct / metabolism
  • Copper / metabolism*
  • Cytosol / metabolism
  • Female
  • Hepatolenticular Degeneration / metabolism*
  • Humans
  • Liver / metabolism*
  • Lysosomes / metabolism*
  • Protein Binding
  • Radioisotopes
  • Subcellular Fractions / metabolism

Substances

  • Radioisotopes
  • Copper